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Keywords: mitochondrial disease
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Biosci Rep (2014) 34 (6): e00151.
Published: 21 November 2014
... aspects of the mitochondrial disease LS (Leigh syndrome), as well as MEFs (mouse embryonic fibroblasts). Although CI structure and function were compromised in all Ndufs4 fky/fky cell types, the mitochondrial membrane potential was selectively impaired in the MEFs, correlating with decreased CI-dependent...
Includes: Supplementary data
Biosci Rep (2007) 27 (1-3): 39–51.
Published: 13 June 2007
... the two genomes and cause diseases that affect mtDNA integrity or expression, being inherited as mendelian traits. © 2007 The Biochemical Society 2007 Mitochondrial disease Mitochondrial DNA mtDNA depletion mtDNA multiple deletions Nucleus-mitochondrion cross-talk ORI GI N A L P A PE R...
Biosci Rep (2007) 27 (1-3): 31–37.
Published: 13 June 2007
...Michelangelo Mancuso; Massimiliano Filosto; Anna Choub; Marta Tentorio; Laura Broglio; Alessandro Padovani; Gabriele Siciliano Mitochondrial diseases are a group of disorders due to a mitochondrial respiratory chain deficiency. They may depend on mitochondrial genome ( mtDNA -related disorders...