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Keywords: Cystic FibrosisClose
Biosci Rep (2022) 42 (7): BSR20212006.
Published: 01 July 2022
...Carlos M. Farinha; Isabelle Callebaut Cystic fibrosis, the most common autosomal recessive disorder in Caucasians, is caused by mutations in the cystic fibrosis transmembrane conductance regulator ( CFTR ) gene, which encodes a cAMP-activated chloride and bicarbonate channel that regulates ion...
Biosci Rep (2006) 26 (1): 55–67.
Published: 15 June 2006
...+Business Media, Inc. 2006 MUC4 Mucins IL-9 Airway epithelium ErbB2 Asthma Cystic fibrosis ORI GIN AL PA PER IL-9 Modulated MUC4 Gene and Glycoprotein Expression in Airway Epithelial Cells Gautam Damera Æ Baoyun Xia Æ Hanumatha R. Ancha Æ Goverdhan P. Sachdev Published online: 19 May 2006...
Biosci Rep (1995) 15 (6): 531–541.
Published: 01 December 1995
...M. A. Gray; J. P. Winpenny; B. Verdon; H. McAlroy; B. E. Argent Cystic fibrosis (CF) affects approximately 1 in 2000 people making it one of the commonest fatal, inherited diseases in the Caucasian population. CF is caused by mutations in a cyclic AMP-regulated chloride channel known as CFTR, which...
Biosci Rep (1990) 10 (6): 563–572.
Published: 01 December 1990
...F. Bertrand; B. Hermelin; A. Paul; I. Garcia; J. Capeau; G. Cherqui; J. Picard In comparison to skin fibroblasts from normal subjects, those from patients with cystic fibrosis (CF): (1) bound [20- 3 H] phorbol 12,13-dibutyrate (PDBu) with a higher affinity (K d =25.8 vs 12.8 nM respectively...
Biosci Rep (1988) 8 (1): 27–33.
Published: 01 February 1988
..., A-kinase) to open apical membrane Cl − channels in CF epithelial cells. Most of the physiological abnormalities of CF including elevated sweat electrolytes and hyperviscous mucus can be explained on this basis. 8 12 1987 © 1988 Plenum Publishing Corporation 1988 cystic fibrosis chloride...
Biosci Rep (1987) 7 (3): 167–185.
Published: 01 March 1987
... fibrosis exocrine autonomic cyclic AMP calcium chloride epithelial Bioscience Reports, Vol. 7, No. 3, 1987 REVIEW The Molecular and Biochemical Basis Cystic Fibrosis Margaret A. McPherson and Robert L. Dormer of Received April 15, 1987 KEY WORDS: cystic fibrosis; exocrine; autonomic; cyclic AMP...